• Rhabdomyosarcoma.
      • It is a highly malignant tumour of the orbit
      • arise from the extraocular muscles. .(MCQ)
      • It is the most common primary orbital tumour among children .(MCQ)
      • usually occurring below the age of 15 years (90%)..(MCQ)
      • Clinical features.
        • It classically presents as rapidly progressive proptosis of sudden onset in a child of 7-8 years
        • The tumour commonly involves the superionasal quadrant .(MCQ)
      • Diagnosis.
        • X- rays showing bone destruction
        • CT scan demonstrating tumour in relation to an extraocular muscle.
        • Diagnosis is confirmed by biopsy.
      • Treatment.
        • High dose radiation therapy  combined with systemic chemotherapy is very effective.
        • Chemotherapy regime consists of Vincristine and actinomycin-D , cyclophosphamide
        • Exenteration is required in a few unresponsive patients.(MCQ)

    Juliana Irina Carver (Battling Alveolar Rhabdomyosarcoma) Part 1
    Juliana was diagnosed with stage 3, group 3 Alveolar Rhabdomyosarcoma on 3/7/07. She had 28 days of radiation therapy and 42 weeks of chemotherapy. She was off treatment for three years with no evidence of disease. She relapsed on 3/17/11 and received another 36 weeks of chemotherapy and 5 more weeks of radiation therapy. Julie relapsed a second time on 6/5/12. She is going to get 12 more rounds of chemo then radiation after the tumors shrink.
    Histopathology Skeletal muscle, face–Alveolar rhabdomyosarcHistopathology Skeletal muscle, face–Alveolar rhabdomyosarcoma
    Cancer – Rhabdomyosarcoma – Treatment and Cure
    Tumor removal (rhabdomyosarcoma)
    Catania, Hospital Vittorio Emanuele, Surgical clinic
    Robotic radical hysterectomy and pelvic lymphadenectomy for uterine rhabdomyosarcoma
    From the Springer article: Robotic radical hysterectomy and pelvic lymphadenectomy for uterine rhabdomyosarcoma