- It is a highly malignant tumour of the orbit
- arise from the extraocular muscles. .(MCQ)
- It is the most common primary orbital tumour among children .(MCQ)
- usually occurring below the age of 15 years (90%)..(MCQ)
- Clinical features.
- It classically presents as rapidly progressive proptosis of sudden onset in a child of 7-8 years
- The tumour commonly involves the superionasal quadrant .(MCQ)
- X- rays showing bone destruction
- CT scan demonstrating tumour in relation to an extraocular muscle.
- Diagnosis is confirmed by biopsy.
- High dose radiation therapy combined with systemic chemotherapy is very effective.
- Chemotherapy regime consists of Vincristine and actinomycin-D , cyclophosphamide
- Exenteration is required in a few unresponsive patients.(MCQ)
Juliana Irina Carver (Battling Alveolar Rhabdomyosarcoma) Part 1
Juliana was diagnosed with stage 3, group 3 Alveolar Rhabdomyosarcoma on 3/7/07. She had 28 days of radiation therapy and 42 weeks of chemotherapy. She was off treatment for three years with no evidence of disease. She relapsed on 3/17/11 and received another 36 weeks of chemotherapy and 5 more weeks of radiation therapy. Julie relapsed a second time on 6/5/12. She is going to get 12 more rounds of chemo then radiation after the tumors shrink.
Histopathology Skeletal muscle, face–Alveolar rhabdomyosarcHistopathology Skeletal muscle, face–Alveolar rhabdomyosarcoma
RESECTION OF THE TUMOR,IBN ALNAFEES TEACHING HOSPITAL
Cancer – Rhabdomyosarcoma – Treatment and Cure
Tumor removal (rhabdomyosarcoma)
Catania, Hospital Vittorio Emanuele, Surgical clinic
Robotic radical hysterectomy and pelvic lymphadenectomy for uterine rhabdomyosarcoma
From the Springer article: Robotic radical hysterectomy and pelvic lymphadenectomy for uterine rhabdomyosarcoma